Leukocyte adhesion deficiency II

Patients have an increased incidence of bacterial infections, persistent leukocytosis, poor pus formation and a number of neurological, developmental and physical abnormalities, typical dysmorphic features, the Bombay (hh) blood phenotype and severe growth and psychomotor retardation. Infections of the skin, lungs, and gums resemble those seen in the moderate type of LAD-1, but the frequency and severity of infections tend to decrease with age.